ODCs

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5 OMIM references -
4 associated genes
1 sign/symptom

COMMON GENES: 1

2 OMIM references -
2 associated genes
8 signs/symptoms

Familial progressive cardiac conduction defect

Hypoplastic left heart syndrome

Citations in the biomedical literature:

Familial progressive cardiac conduction defect		Hypoplastic left heart syndrome
	Synonym(s): - Familial LenÃ¨gre disease - Familial Lev disease - Familial Lev-LenÃ¨gre disease - Familial PCCD - Familial progressive heart block - Hereditary bundle branch defect		Synonym(s): (no synonyms)

	Classification (Orphanet): - Rare cardiac disease - Rare genetic disease		Classification (Orphanet): - Rare developmental defect during embryogenesis - Rare surgical cardiac disease

	Classification (ICD10): - Diseases of the circulatory system -		Classification (ICD10): - Congenital malformations, deformations and chromosomal abnormalities -

	Epidemiological data: Class of prevalence: <1 / 1 000 000 Average age onset: adulthood Average age of death: elderly Type of inheritance: autosomal dominant		Epidemiological data: Class of prevalence: unknown Average age onset: neonatal/infancy Average age of death: - Type of inheritance: unknown

	External references: 5 OMIM references - No MeSH references		External references: 2 OMIM references - 1 MeSH reference: D018636

Familial progressive cardiac conduction defect		Hypoplastic left heart syndrome
	Frequent - Cardiac rhythm disorder / arrhythmia		Very frequent - Hypoplastic left heart / ventricle - Stillbirth / neonatal death Frequent - Hypoplastic aorta / coarctation / stenosis / anomaly / aortic arch interruption Occasional - Atrial septal defect / interauricular communication - Maternal diabetes - Mitral valve prolapse / incompetence / insufficiency / regurgitation / ring anomaly - Patent ductus arteriosus - Total / partial trisomy / duplication